Cruveilhier–Baumgarten disease


Cruveilhier–Baumgarten disease or Pégot-Cruveilhier–Baumgarten disease is a rare medical condition in which the umbilical or paraumbilical veins are distended, with an abdominal wall bruit and palpable thrill, portal hypertension with splenomegaly, hypersplenism and oesophageal varices, with a normal or small liver. The presence of the Cruveilhier-Baumgarten venous hum is highly suggestive of portal hypertension, and is never a normal physical examination finding.
It was first described by Pégot in 1833, and then by Jean Cruveilhier and Paul Clemens von Baumgarten.
Armstrong et al. and Steinburg and Galambos described two different types of the condition: